The hemophagocytic syndrome
DOI:
https://doi.org/10.5377/rmh.v86i3-4.12179Keywords:
Bone marrow, Hemophagocytic Iymphohistiocytosis, Phagocytosis, SeverityAbstract
Background: The hemophagocytic syndrome (SH) is a syndrome of pathological immune activation, rare, little diagnosed, its importance lies in its severity, since they are very aggressive cases that evolve in a short time in a fulminating way, with a lethal multiorgan failure, before establish a diagnosis. They are found in all age groups, but in general it is more frequent in children. The purpose of the revision was to obtain information about this pathology, identify the condition in a timely manner and also administer an early and adequate treatment to improve patient survival. Methods: We carried out an exhaustive search of articles with less than 10 years of publication in the PubMed, Scielo, Elsevier, Scribd, Medigraphic databases. Development and conclusions: Although SH is difficult to identify due to nonspecific symptoms, if it is diagnosed and treated at the opportune moment, given its high morbidity and mortality, it will be possible to save many lives.
Downloads
221